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Polymers of Z α1-antitrypsin are secreted in cell models of disease.

Accepted version
Peer-reviewed

Type

Article

Change log

Authors

Fra, Annamaria 
Cosmi, Francesca 
Ordoñez, Adriana 
Berardelli, Romina 
Perez, Juan 

Description

Keywords

Alleles, Biological Transport, HEK293 Cells, Humans, Immunologic Factors, Mutation, Protein Multimerization, alpha 1-Antitrypsin, alpha 1-Antitrypsin Deficiency

Journal Title

Eur Respir J

Conference Name

Journal ISSN

0903-1936
1399-3003

Volume Title

47

Publisher

European Respiratory Society (ERS)
Sponsorship
Medical Research Council (G0901786)
Medical Research Council (G1002610)
Medical Research Council (G0601840)