Polymers of Z α1-antitrypsin are secreted in cell models of disease.
Accepted version
Peer-reviewed
Repository URI
Repository DOI
Change log
Authors
Description
Keywords
Alleles, Biological Transport, HEK293 Cells, Humans, Immunologic Factors, Mutation, Protein Multimerization, alpha 1-Antitrypsin, alpha 1-Antitrypsin Deficiency
Journal Title
Eur Respir J
Conference Name
Journal ISSN
0903-1936
1399-3003
1399-3003
Volume Title
47
Publisher
European Respiratory Society (ERS)
Publisher DOI
Sponsorship
Medical Research Council (G0901786)
Medical Research Council (G1002610)
Medical Research Council (G0601840)
Medical Research Council (G1002610)
Medical Research Council (G0601840)