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Early loss of Crebbp confers malignant stem cell properties on lymphoid progenitors.

Accepted version
Peer-reviewed

Type

Article

Change log

Authors

Horton, Sarah J 
Giotopoulos, George  ORCID logo  https://orcid.org/0000-0003-1390-6592
Yun, Haiyang 
Vohra, Shabana 
Sheppard, Olivia 

Abstract

Loss-of-function mutations of cyclic-AMP response element binding protein, binding protein (CREBBP) are prevalent in lymphoid malignancies. However, the tumour suppressor functions of CREBBP remain unclear. We demonstrate that loss of Crebbp in murine haematopoietic stem and progenitor cells (HSPCs) leads to increased development of B-cell lymphomas. This is preceded by accumulation of hyperproliferative lymphoid progenitors with a defective DNA damage response (DDR) due to a failure to acetylate p53. We identify a premalignant lymphoma stem cell population with decreased H3K27ac, which undergoes transcriptional and genetic evolution due to the altered DDR, resulting in lymphomagenesis. Importantly, when Crebbp is lost later in lymphopoiesis, cellular abnormalities are lost and tumour generation is attenuated. We also document that CREBBP mutations may occur in HSPCs from patients with CREBBP-mutated lymphoma. These data suggest that earlier loss of Crebbp is advantageous for lymphoid transformation and inform the cellular origins and subsequent evolution of lymphoid malignancies.

Description

Keywords

Acetylation, Animals, CREB-Binding Protein, Cell Proliferation, Cell Self Renewal, Cell Transformation, Neoplastic, Cells, Cultured, DNA Damage, Epigenesis, Genetic, Gene Expression Regulation, Neoplastic, Genetic Predisposition to Disease, Histones, Lymphangiogenesis, Lymphoid Progenitor Cells, Lymphoma, Lymphopoiesis, Methylation, Mice, Mice, Inbred C57BL, Mice, Knockout, Mutation, Neoplastic Stem Cells, Phenotype, Signal Transduction, Time Factors, Transcription, Genetic, Tumor Suppressor Protein p53

Journal Title

Nat Cell Biol

Conference Name

Journal ISSN

1465-7392
1476-4679

Volume Title

19

Publisher

Springer Science and Business Media LLC
Sponsorship
Medical Research Council (MC_PC_12009)
Wellcome Trust (106068/Z/14/Z)
Medical Research Council (MR/M008975/1)
Medical Research Council (MR/M010392/1)
European Research Council (647685)
Wellcome Trust (109967/Z/15/Z)
Medical Research Council (MR/M008584/1)
Wellcome Trust (097922/Z/11/Z)
Wellcome Trust (100140/Z/12/Z)
Worldwide Cancer Research (None)
Medical Research Council (MR/L019027/1)
Wellcome Trust (096956/Z/11/Z)