New perspectives in eosinophilic granulomatosis with polyangiitis (EGPA): report of the first meeting of the European EGPA Study Group.
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Authors
Marvisi, Chiara
Sinico, Renato Alberto
Salvarani, Carlo
Prisco, Domenico
Terrier, Benjamin
Vaglio, Augusto
European EGPA Study Group,
Publication Date
2019-11Journal Title
Internal and emergency medicine
ISSN
1828-0447
Publisher
Springer Nature
Volume
14
Issue
8
Pages
1193-1197
Language
eng
Type
Article
This Version
AM
Physical Medium
Print-Electronic
Metadata
Show full item recordCitation
Marvisi, C., Sinico, R. A., Salvarani, C., Jayne, D., Prisco, D., Terrier, B., Emmi, G., et al. (2019). New perspectives in eosinophilic granulomatosis with polyangiitis (EGPA): report of the first meeting of the European EGPA Study Group.. Internal and emergency medicine, 14 (8), 1193-1197. https://doi.org/10.1007/s11739-019-02166-5
Abstract
The European Eosinophilic Granulomatosis with Polyangiitis (EGPA) study group first gathered in Firenze in December 2018. The discussion was centred around the clinical and therapeutic needs in EGPA which still remain unmet. Indeed, EGPA is a puzzling and rare disease which shares clinical features with other anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAVs) and hypereosinophilic syndromes (HESs). Some of the recommendations published in 2015 are based on data derived from EGPA-related diseases, rather than from EGPA itself, and therefore need to be updated. Thus, the aim of the meeting was to stimulate ongoing research, to promote collaborative European studies and to define the main issues on which future studies should be focused. Current fields of research on EGPA include potential serological biomarkers of disease activity and of specific organ involvement, possible links between different genetic variants and clinical phenotypes, and new therapeutic perspectives. Herein, we give an overview of the meeting with the goal to stimulate an international collaboration and new points of discussion.
Keywords
European EGPA Study Group, Humans, Eosinophilic Granuloma, Consensus, Europe, Granulomatosis with Polyangiitis
Identifiers
External DOI: https://doi.org/10.1007/s11739-019-02166-5
This record's URL: https://www.repository.cam.ac.uk/handle/1810/305820
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